Sturge-Weber syndrome and associated congenital vascular disorders: A review

Nirmal Nathan, Seth Thaller

Research output: Contribution to journalArticle

11 Citations (Scopus)

Abstract

Sturge-Weber syndrome (SWS), Klippel-Trenaunay syndrome (KTS), and Parkes-Weber syndrome (PWS) represent a wide range of congenital vascular abnormality syndromes. Although many of the diagnostic criteria overlap for these syndromes, there are important differences among these diseases that carry important prognostic and therapeutic implications. This review attempts to clearly distinguish among SWS, KTS, and PWS, although loosely categorizing them as a family of congenital vascular disorders. A review of literature reveals that a variety of diagnostic tools exist that can help differentiate between the syndromes and assess risk for certain complications, which may help tailor various treatment modalities for a particular patient.

Original languageEnglish
Pages (from-to)724-728
Number of pages5
JournalJournal of Craniofacial Surgery
Volume17
Issue number4
DOIs
StatePublished - Jul 1 2006

Fingerprint

Sturge-Weber Syndrome
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Blood Vessels
Klippel-Trenaunay-Weber Syndrome
Therapeutics
Weber Klippel Trenaunay

Keywords

  • Angiomatosis
  • Congenital vascular disorder
  • Hemagioma
  • Klippel-Trenaunay Syndrome (KTS)
  • Parkes-Weber Syndrome (PWS)
  • Port-wine stain
  • Sturge-Weber Syndrome (SWS)

ASJC Scopus subject areas

  • Surgery

Cite this

Sturge-Weber syndrome and associated congenital vascular disorders : A review. / Nathan, Nirmal; Thaller, Seth.

In: Journal of Craniofacial Surgery, Vol. 17, No. 4, 01.07.2006, p. 724-728.

Research output: Contribution to journalArticle

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