TY - JOUR
T1 - Pseudoxanthoma Elasticum with Severe Cardiovascular Disease in a Child
AU - Schachner, Lawrence
AU - Young, Dennison
PY - 1974/4
Y1 - 1974/4
N2 - A 13-year-old girl was hospitalized for a second episode of acute upper gastrointestinal hemorrhage. Acute inferior wall myocardial and diffuse subendocardial infarction was diagnosed on the fifth hospital day. Clinical and pathological evaluation established a diagnosis of pseudoxanthoma elasticum (PXE) with characteristic dermatological, ophthalmological, gastrointestinal, and peripheral vascular involvement. Recovery from the myocardial infarction was uneventful despite the development of severe systemic hypertension. Although PXE is a relatively uncommon disease and often seemingly benign, it may be responsible for acute catastrophic events such as gastrointestinal hemorrhage, myocardial infarction, and sudden death in the young.
AB - A 13-year-old girl was hospitalized for a second episode of acute upper gastrointestinal hemorrhage. Acute inferior wall myocardial and diffuse subendocardial infarction was diagnosed on the fifth hospital day. Clinical and pathological evaluation established a diagnosis of pseudoxanthoma elasticum (PXE) with characteristic dermatological, ophthalmological, gastrointestinal, and peripheral vascular involvement. Recovery from the myocardial infarction was uneventful despite the development of severe systemic hypertension. Although PXE is a relatively uncommon disease and often seemingly benign, it may be responsible for acute catastrophic events such as gastrointestinal hemorrhage, myocardial infarction, and sudden death in the young.
UR - http://www.scopus.com/inward/record.url?scp=0016051736&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=0016051736&partnerID=8YFLogxK
U2 - 10.1001/archpedi.1974.02110230117021
DO - 10.1001/archpedi.1974.02110230117021
M3 - Article
C2 - 4544975
AN - SCOPUS:0016051736
VL - 127
SP - 571
EP - 575
JO - A.M.A. American journal of diseases of children
JF - A.M.A. American journal of diseases of children
SN - 2168-6203
IS - 4
ER -