Neuro-Behcet Disease Mimicking Lymphoma of the Brain and Coexisting with A Dural Arteriovenous Fistula: A Case Report

Valeria Ripa, Churl Su Kwon, Joshua D. Burks, Jacques J. Morcos

Research output: Contribution to journalArticle


Background: Diverse clinical manifestations have characterized reports of central nervous system involvement in Behcet disease. There is a limited number of published case reports of neuro-Behcet disease mimicking brain tumor. Case Description: We present a rare case of neuro-Behcet disease exhibiting mixed systemic and neurological symptoms mimicking malignant lymphoma. Delayed presentation of oral aphthae and rapid improvement of symptoms with steroid treatment led to a diagnosis of neuro-Behcet disease without brain biopsy. The patient also underwent surgery for the resection of an arterio-venous fistula. Conclusions: We recommend management of neuro-Behcet disease based on perceived natural history risks, with the understanding that no data exist on this within patients population. A multidisciplinary team approach is always recommended because neuro-Behcet disease is an uncommon condition, especially in neurosurgical practice.

Original languageEnglish (US)
Pages (from-to)205-211
Number of pages7
JournalWorld neurosurgery
StatePublished - Jan 2020
Externally publishedYes



  • Arterio-venous fistula
  • Brain lymphoma-like lesions
  • Neuro-Behcet disease

ASJC Scopus subject areas

  • Surgery
  • Clinical Neurology

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