Kaposiform hemangioendothelioma is a rare locally aggressive vascular tumor that usually manifests during early childhood. Typically the lesion presents with skin, soft tissue and bone involvement and is characterized histologically by ill-defined nodularity and the presence of spindle cells with resemblance to Kaposi's sarcoma. We report a rare neonatal case of a splenic kaposiform hemangioendothelioma associated with Kasabach-Merritt phenomenon that was diagnosed with radiographic imaging. Because of the rapid onset of thrombocytopenia and anemia, the patient required urgent splenectomy with subsequent resolution of the blood dyscrasias.
- Kaposiform hemangioendothelioma
- Kasabach-Merritt phenomenon
- Neonatal kaposiform hemangioendothelioma
- Splenic mass
- Vascular tumor
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health