Neonatal kaposiform hemangioendothelioma of the spleen associated with Kasabach-Merritt phenomenon

Samuel A. Shabtaie, Bo Wang, Mark Owyong, Catalina Ruiz-Mesa, Fernando Corrales-Medina, Claudia P. Rojas, Juan C. Infante, Holly Neville, Eduardo Perez, Juan E Sola, Anthony Richard Hogan

Research output: Contribution to journalArticle

3 Scopus citations

Abstract

Kaposiform hemangioendothelioma is a rare locally aggressive vascular tumor that usually manifests during early childhood. Typically the lesion presents with skin, soft tissue and bone involvement and is characterized histologically by ill-defined nodularity and the presence of spindle cells with resemblance to Kaposi's sarcoma. We report a rare neonatal case of a splenic kaposiform hemangioendothelioma associated with Kasabach-Merritt phenomenon that was diagnosed with radiographic imaging. Because of the rapid onset of thrombocytopenia and anemia, the patient required urgent splenectomy with subsequent resolution of the blood dyscrasias.

Original languageEnglish (US)
Pages (from-to)1047-1050
Number of pages4
JournalJournal of Pediatric Surgery
Volume51
Issue number6
DOIs
StatePublished - Jun 1 2016

Keywords

  • Kaposiform hemangioendothelioma
  • Kasabach-Merritt phenomenon
  • Neonatal kaposiform hemangioendothelioma
  • Splenic mass
  • Vascular tumor

ASJC Scopus subject areas

  • Surgery
  • Pediatrics, Perinatology, and Child Health

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