Abstract
Kaposiform hemangioendothelioma is a rare locally aggressive vascular tumor that usually manifests during early childhood. Typically the lesion presents with skin, soft tissue and bone involvement and is characterized histologically by ill-defined nodularity and the presence of spindle cells with resemblance to Kaposi's sarcoma. We report a rare neonatal case of a splenic kaposiform hemangioendothelioma associated with Kasabach-Merritt phenomenon that was diagnosed with radiographic imaging. Because of the rapid onset of thrombocytopenia and anemia, the patient required urgent splenectomy with subsequent resolution of the blood dyscrasias.
Original language | English (US) |
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Pages (from-to) | 1047-1050 |
Number of pages | 4 |
Journal | Journal of Pediatric Surgery |
Volume | 51 |
Issue number | 6 |
DOIs | |
State | Published - Jun 1 2016 |
Keywords
- Kaposiform hemangioendothelioma
- Kasabach-Merritt phenomenon
- Neonatal kaposiform hemangioendothelioma
- Splenic mass
- Vascular tumor
ASJC Scopus subject areas
- Surgery
- Pediatrics, Perinatology, and Child Health