Sclerodermia lineare a 'colpo di sciabola': Presentazione di un caso e revisione della letteratura

Translated title of the contribution: Linear scleroderma 'en coup de sabre': Description of a case and review of the literature

A. Tosti, M. Iorizzo, B. M. Piraccini, S. Lorenzi, C. Vincenzi

Research output: Contribution to journalArticle

1 Scopus citations

Abstract

Scleroderma 'en coup de sabre' is a form of linear scleroderma characterized by a sclerotic band involving the face and the scalp with an area of cicatricial alopecia. It is a typical childhood disease affecting most commonly caucasian females. The cause remains unknown and the pathogenesis is still uncertain. It seems that a genetical predisposition maybe at the basis of this disease and that, a trauma or an autoimmune activation, can provoke clinical manifestations. The current theories regarding the pathogenesis of linear scleroderma, from the immune disorders to vascular abnormalities, are described. A 20-year-old patient affected by linear scleroderma 'en coup de sabre', who was successfully treated with oral calcitriol for 8 months, is presented.

Translated title of the contributionLinear scleroderma 'en coup de sabre': Description of a case and review of the literature
Original languageItalian
Pages (from-to)487-489
Number of pages3
JournalGiornale Italiano di Dermatologia e Venereologia
Volume135
Issue number4
StatePublished - Jan 1 2000
Externally publishedYes

Keywords

  • Alopecia
  • Calcitriol therapeutic use
  • Scleroderma, circums ribed

ASJC Scopus subject areas

  • Dermatology

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