Left isomerism and complete atrioventricular block: A report of six cases

Otto L. Garcia, Ashok V. Mehta, Arthur S. Pickoff, Dolores F. Tamer, Pedro L. Ferrer, Grace S. Wolff, Henry Gelband

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35 Scopus citations

Abstract

Six children, aged 12 days to 13 years, with left isomerism and complete atrioventricular (A-V) block are presented. In all six patients the diagnosis of left isomerism was suggested by an interrupted inferior vena cava found during cardiac catheterization and angiocardiography;four patients had complex heart disease consisting of endocardial cushion defect, five had a common atrium, three had pulmonary stenosis, three had patent ductus arteriosus and two had dextrocardia. Further anatomic abnormalities included situs inversus of the viscera (four patients) as well as partial malrotation of the bowel. Of the six patients, four had congenital complete A-V block, whereas the remaining two had A-V conduction disturbances documented during early infancy that progressed to complete A-V block later in life. All six patients required pacemaker implantation and five of the six patients died. This report discusses the clinical presentation of complete A-V block and left isomerism and reviews the literature.

Original languageEnglish (US)
Pages (from-to)1103-1107
Number of pages5
JournalThe American Journal of Cardiology
Volume48
Issue number6
DOIs
StatePublished - Dec 1981

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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    Garcia, O. L., Mehta, A. V., Pickoff, A. S., Tamer, D. F., Ferrer, P. L., Wolff, G. S., & Gelband, H. (1981). Left isomerism and complete atrioventricular block: A report of six cases. The American Journal of Cardiology, 48(6), 1103-1107. https://doi.org/10.1016/0002-9149(81)90327-1