Clear cell sarcoma of the kidney (CCSK) is a rare tumor. It has a wide histologic spectrum and often mimics other pediatric renal tumors, resulting in considerable diagnostic difficulty.We report the case of a two-year-old who presented with a large (14 cm) abdominal mass. Prior to neoadjuvant chemotherapy, a biopsy was performed, which revealed Wilms tumor. The final pathology diagnosis at the time of resection revealed CCSK.
- Clear cell sarcoma
- Wilms tumor
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health