Kaposiform hemangioendothelioma associated with nonimmune fetal hydrops

Antonio E. Martinez, Morton J. Robinson, John B. Alexis

Research output: Contribution to journalArticlepeer-review

21 Scopus citations


We describe the case of a 31-week fetus who died in utero with an invasive retroperitoneal kaposiform hemangioendothelioma. This rare vascular neoplasm usually presents as a localized violaceous skin lesion in infants and behaves in a benign fashion; however, kaposiform hemangioendothelioma may present as an invasive neoplasm of the chest or abdominal cavity, where it can lead to the Kasabach-Merritt syndrome, which consists of thrombocytopenia, consumptive coagulopathy, and microangiopathic anemia in association with a vascular anomaly. The case we describe is unique in that the tumor presented in utero and led to intrauterine nonimmune fetal hydrops. Kaposiform hemangioendothelioma has been described in utero; however, to our knowledge, intrauterine fetal death as a direct consequence has not been reported previously in the literature.

Original languageEnglish (US)
Pages (from-to)678-681
Number of pages4
JournalArchives of Pathology and Laboratory Medicine
Issue number6
StatePublished - Dec 1 2004

ASJC Scopus subject areas

  • Pathology and Forensic Medicine
  • Medical Laboratory Technology


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