Infantile Myofibromatosis: A Case Report

Betty Bellman, George Wooming, Larry Landsman, Neal Penneys, Lawrence A. Schachner

Research output: Contribution to journalArticle

12 Scopus citations

Abstract

A male infant had three nodules on the left cheek, right forearm, and right neck. Biopsy specimen revealed infantile myofibromatosis (IM). Further evaluation revealed a solitary pulmonary nodule in the right middle lobe located far from mediastinal structures, which had no evidence of tumor enlargement on follow-up tomographic scan. Immunoperoxidase studies were negative for desmin and positive for actin. This is a potentially life-threatening multiorgan system disease; however, if lesions are limited mainly to the skin and soft tissues, the prognosis becomes more favorable. Although many reports suggest spontaneous and complete healing of the cutaneous lesions, our patient had profound atrophy at lesion sites as resolution occurred.

Original languageEnglish (US)
Pages (from-to)306-309
Number of pages4
JournalPediatric Dermatology
Volume8
Issue number4
DOIs
StatePublished - Dec 1991

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Dermatology

Fingerprint Dive into the research topics of 'Infantile Myofibromatosis: A Case Report'. Together they form a unique fingerprint.

  • Cite this