Fucosidosis: Ultrastructural study of the eye in an adult

Motohiro Hoshino, Terrence O'Brien, Jan M. McDonnell, Zenaida C. de la Cruz, W. Richard Green

Research output: Contribution to journalArticle

5 Citations (Scopus)

Abstract

The ocular histopathological and ultrastructural features of fucosidosis in a man who survived to the age of 25 years are reported. Virtually all of the cells of the eye contained cytoplasmic, membrane-bound, and confluent areas of fibrillogranular and multilaminated material. The most striking accumulations were present within the endothelial cells lining blood vessels and corneal endothelium, and the least amount was present in the uveal melanocytes.

Original languageEnglish
Pages (from-to)162-171
Number of pages10
JournalGraefe's Archive for Clinical and Experimental Ophthalmology
Volume227
Issue number2
DOIs
StatePublished - Mar 1 1989
Externally publishedYes

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Fucosidosis
Corneal Endothelium
Melanocytes
Blood Vessels
Endothelial Cells
Cell Membrane

ASJC Scopus subject areas

  • Ophthalmology

Cite this

Fucosidosis : Ultrastructural study of the eye in an adult. / Hoshino, Motohiro; O'Brien, Terrence; McDonnell, Jan M.; de la Cruz, Zenaida C.; Green, W. Richard.

In: Graefe's Archive for Clinical and Experimental Ophthalmology, Vol. 227, No. 2, 01.03.1989, p. 162-171.

Research output: Contribution to journalArticle

Hoshino, Motohiro ; O'Brien, Terrence ; McDonnell, Jan M. ; de la Cruz, Zenaida C. ; Green, W. Richard. / Fucosidosis : Ultrastructural study of the eye in an adult. In: Graefe's Archive for Clinical and Experimental Ophthalmology. 1989 ; Vol. 227, No. 2. pp. 162-171.
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