Fibrous dysplasia in combination with aneurysmal bone cyst of the occipital bone and the clivus: Case report and review of the literature

Eyal Itshayek, Sergey Spector, Moshe Gomori, Ricardo Segal, Jack P. Rock, Ronald Benveniste, Martin B. Camins, Jacques Brotchi

Research output: Contribution to journalArticlepeer-review

37 Scopus citations

Abstract

OBJECTIVE AND IMPORTANCE: Fibrous dysplasia of the cranium is a relatively uncommon disorder that affects primarily the anterior cranial region; its occurrence in the cranial base in combination with aneurysmal bone cyst (ABC) constitutes an extremely rare condition, only two cases of which have been reported previously in the literature. It is important to recognize and treat these cases properly because of the special location in the cranial base and the possibility of neural structure impingement. CLINICAL PRESENTATION: We report the case of a 19-year-old man with a slowly enlarging mass of the occiput, with computed tomographic and magnetic resonance imaging revealing involvement of petrous and basisphenoid bone and growing ABC. INTERVENTION: Open biopsy confirmed the diagnosis of fibrous dysplasia. Partial excision of the lesion and removal of the ABC were performed in a second stage after embolization. CONCLUSION: ABC associated with fibrous dysplasia of the cranial base may enlarge rapidly after puberty and require excision. This is facilitated by preoperative embolization.

Original languageEnglish (US)
Pages (from-to)815-818
Number of pages4
JournalNeurosurgery
Volume51
Issue number3
DOIs
StatePublished - Sep 1 2002
Externally publishedYes

Keywords

  • Aneurysmal bone cyst
  • Basisphenoid bone
  • Cranial base surgery
  • Fibrous dysplasia
  • Petrous bone
  • Preoperative embolization

ASJC Scopus subject areas

  • Clinical Neurology
  • Surgery

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