Epithelial–Myoepithelial Carcinoma Presenting as a Pseudo Veno-Lymphatic Malformation

Emily Li, Alberto Distefano, John Sinard, Amanda Wong, Renelle Pointdujour-Lim

Research output: Contribution to journalArticlepeer-review

1 Scopus citations


A 41-year-old woman presented with several days of right eye pain and blurred vision. Examination and radiologic workup were consistent with a veno-lymphatic malformation, including demonstration of cystic fluid–fluid levels on imaging. Histopathology supported the presence of cystic spaces but revealed the final diagnosis of lacrimal epithelial–myoepithelial carcinoma, a rare neoplasm typically associated with the salivary gland. This represents the first reported case of lacrimal epithelial–myoepithelial carcinoma presenting with pain and evidence of intralesional cysts on radiographic and histopathologic evaluation. Better characterization will enable recognition, complete surgical excision, and potential adjuvant radiation therapy.

Original languageEnglish (US)
Pages (from-to)E157-E160
JournalOphthalmic plastic and reconstructive surgery
Issue number5
StatePublished - Sep 1 2018

ASJC Scopus subject areas

  • Surgery
  • Ophthalmology


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