Epidermolysis bullosa dystrophica polydysplastica. A case of anesthetic management in oral surgery

Manuel M. Album, Allen Gaisin, K. W.Terry Lee, Billy Eugene Buck, William G. Sharrar, Frances Mc N. Gill

Research output: Contribution to journalArticle

14 Scopus citations

Abstract

Epidermolysis bullosa dystrophica is a rare disease that affects the skin and mucous membranes. Manifest at birth, it is characterized by poor dentition, esophageal strictures, syndactyly, and severe chronic anemia. Our 12-year-old patient required extensive dental treatment which necessitated overcoming problems of anesthesia as well as developing a technique of management that provided maximum safety and a minimum of discomfort. Transmission electron microscopy of sections of the gingiva revealed possible degenerative collagen fibers and an interrupted basement membrane. Anchoring fibrils normally found in the connective tissue beneath the epithelium were absent.

Original languageEnglish (US)
Pages (from-to)859-872
Number of pages14
JournalOral Surgery, Oral Medicine, Oral Pathology
Volume43
Issue number6
DOIs
StatePublished - Jun 1977

ASJC Scopus subject areas

  • Pathology and Forensic Medicine
  • Dentistry(all)

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