Clinical presentation of fibrodysplasia ossificans progressiva: Pitfalls in diagnosis

Christopher J. Magryta, Chris J. Kligora, H. Thomas Temple, Rajesh K. Malik

Research output: Contribution to journalArticle

11 Citations (Scopus)

Abstract

A patient presented with a rapidly growing mass in the cervicothoracic paraspinous region. Associated clinical and radiographic skeletal abnormalities and histopathologic findings showing mild to moderate proliferation of spindle cells in a myxoid stroma led to the diagnosis of fibrodysplasia ossificans progressiva. Recognizing the clinical features of this disease is important and should avoid the need for obtaining tissue to make the diagnosis, because performing a biopsy may be particularly morbid in these patients.

Original languageEnglish
Pages (from-to)539-543
Number of pages5
JournalJournal of Pediatric Hematology/Oncology
Volume21
Issue number6
DOIs
StatePublished - Nov 1 1999

Fingerprint

Myositis Ossificans
Cell Proliferation
Biopsy

Keywords

  • Fibrodysplasia ossificans progressiva
  • Paraspinous mass

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Oncology
  • Hematology

Cite this

Clinical presentation of fibrodysplasia ossificans progressiva : Pitfalls in diagnosis. / Magryta, Christopher J.; Kligora, Chris J.; Thomas Temple, H.; Malik, Rajesh K.

In: Journal of Pediatric Hematology/Oncology, Vol. 21, No. 6, 01.11.1999, p. 539-543.

Research output: Contribution to journalArticle

Magryta, Christopher J. ; Kligora, Chris J. ; Thomas Temple, H. ; Malik, Rajesh K. / Clinical presentation of fibrodysplasia ossificans progressiva : Pitfalls in diagnosis. In: Journal of Pediatric Hematology/Oncology. 1999 ; Vol. 21, No. 6. pp. 539-543.
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