Abstract
Congenital agenesis of the sternum is an extremely unusual malformation rarely encountered by the practicing Otolaryngologist. It typically arises in conjunction with other midline ventral congenital anomalies, including abdominal, diaphragmatic, and cardiac malformations. We report a case series of two patients managed with tracheotomy placement due to prolonged intubation. The first patient was a 63-day-old infant born at 34 weeks gestation with dysmorphic features, cleft lip and palate, and skeletal dysplasia, including absence of the sternum. The second patient was a 31-day-old infant born with ectopic cordis and diaphragmatic hernia. The inadequate closure of the anterior chest wall secondary to manubrium malformation or a variant contributes significantly to a child's inability to generate adequate ventilatory pressures. As a result, airway management must be considered not only to ensure airway patency but also an appropriate physiological environment to allow for adequate air exchange in the lungs.
| Original language | English |
|---|---|
| Pages (from-to) | 364-367 |
| Number of pages | 4 |
| Journal | American Journal of Otolaryngology - Head and Neck Medicine and Surgery |
| Volume | 31 |
| Issue number | 5 |
| DOIs | |
| State | Published - Sep 1 2010 |
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ASJC Scopus subject areas
- Otorhinolaryngology
Cite this
Airway implications of congenital sternal agenesis. / Vivero, Richard J.; Fort, Alexander; Ruiz, Jose; Roy, Soham.
In: American Journal of Otolaryngology - Head and Neck Medicine and Surgery, Vol. 31, No. 5, 01.09.2010, p. 364-367.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Airway implications of congenital sternal agenesis
AU - Vivero, Richard J.
AU - Fort, Alexander
AU - Ruiz, Jose
AU - Roy, Soham
PY - 2010/9/1
Y1 - 2010/9/1
N2 - Congenital agenesis of the sternum is an extremely unusual malformation rarely encountered by the practicing Otolaryngologist. It typically arises in conjunction with other midline ventral congenital anomalies, including abdominal, diaphragmatic, and cardiac malformations. We report a case series of two patients managed with tracheotomy placement due to prolonged intubation. The first patient was a 63-day-old infant born at 34 weeks gestation with dysmorphic features, cleft lip and palate, and skeletal dysplasia, including absence of the sternum. The second patient was a 31-day-old infant born with ectopic cordis and diaphragmatic hernia. The inadequate closure of the anterior chest wall secondary to manubrium malformation or a variant contributes significantly to a child's inability to generate adequate ventilatory pressures. As a result, airway management must be considered not only to ensure airway patency but also an appropriate physiological environment to allow for adequate air exchange in the lungs.
AB - Congenital agenesis of the sternum is an extremely unusual malformation rarely encountered by the practicing Otolaryngologist. It typically arises in conjunction with other midline ventral congenital anomalies, including abdominal, diaphragmatic, and cardiac malformations. We report a case series of two patients managed with tracheotomy placement due to prolonged intubation. The first patient was a 63-day-old infant born at 34 weeks gestation with dysmorphic features, cleft lip and palate, and skeletal dysplasia, including absence of the sternum. The second patient was a 31-day-old infant born with ectopic cordis and diaphragmatic hernia. The inadequate closure of the anterior chest wall secondary to manubrium malformation or a variant contributes significantly to a child's inability to generate adequate ventilatory pressures. As a result, airway management must be considered not only to ensure airway patency but also an appropriate physiological environment to allow for adequate air exchange in the lungs.
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UR - http://www.scopus.com/inward/citedby.url?scp=77956229784&partnerID=8YFLogxK
U2 - 10.1016/j.amjoto.2009.04.010
DO - 10.1016/j.amjoto.2009.04.010
M3 - Article
C2 - 20015780
AN - SCOPUS:77956229784
VL - 31
SP - 364
EP - 367
JO - American Journal of Otolaryngology - Head and Neck Medicine and Surgery
JF - American Journal of Otolaryngology - Head and Neck Medicine and Surgery
SN - 0196-0709
IS - 5
ER -