Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease: A case report

Marjorie Gayanilo; Michael Nares; Ofelia Alvarez; Sethuraman Swaminathan

doi:10.1097/01.mph.0000438028.87141.8c

Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease: A case report

Marjorie Gayanilo, Michael Nares, Ofelia Alvarez, Sethuraman Swaminathan

Pediatrics

Research output: Contribution to journal › Article › peer-review

Abstract

Hemoglobin SC (HbSC) disease is the second most common inherited disorder of hemoglobin, in which there is a coinheritance of mutated b globin genes resulting in hemoglobin S and hemoglobin C.1 HbSC is less severe than the homozygous HbSS disease but some complications can be equally severe. Acute myocardial ischemia and infarction have been reported on rare occasions in children with HbSS disease. However, this complication is not reported in children with HbSC disease. We report one such case of acute myocardial ischemia in an adolescent with HbSC disease, in association with acute chest syndrome.

Original language	English (US)
Pages (from-to)	e97-e99
Journal	Journal of Pediatric Hematology/Oncology
Volume	36
Issue number	2
DOIs	https://doi.org/10.1097/01.mph.0000438028.87141.8c
State	Published - Mar 1 2014

Keywords

hemoglobin SC
myocardial ischemia
sickle cell crisis

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Oncology
Hematology

Access to Document

10.1097/01.mph.0000438028.87141.8c

Fingerprint Dive into the research topics of 'Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease: A case report'. Together they form a unique fingerprint.

Cite this

@article{1ec140d04cee431f9b0abae39ca53af8,

title = "Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease: A case report",

abstract = "Hemoglobin SC (HbSC) disease is the second most common inherited disorder of hemoglobin, in which there is a coinheritance of mutated b globin genes resulting in hemoglobin S and hemoglobin C.1 HbSC is less severe than the homozygous HbSS disease but some complications can be equally severe. Acute myocardial ischemia and infarction have been reported on rare occasions in children with HbSS disease. However, this complication is not reported in children with HbSC disease. We report one such case of acute myocardial ischemia in an adolescent with HbSC disease, in association with acute chest syndrome.",

keywords = "hemoglobin SC, myocardial ischemia, sickle cell crisis",

author = "Marjorie Gayanilo and Michael Nares and Ofelia Alvarez and Sethuraman Swaminathan",

year = "2014",

month = mar,

day = "1",

doi = "10.1097/01.mph.0000438028.87141.8c",

language = "English (US)",

volume = "36",

pages = "e97--e99",

journal = "Journal of Pediatric Hematology/Oncology",

issn = "1077-4114",

publisher = "Lippincott Williams and Wilkins",

number = "2",

}

TY - JOUR

T1 - Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease

T2 - A case report

AU - Gayanilo, Marjorie

AU - Nares, Michael

AU - Alvarez, Ofelia

AU - Swaminathan, Sethuraman

PY - 2014/3/1

Y1 - 2014/3/1

N2 - Hemoglobin SC (HbSC) disease is the second most common inherited disorder of hemoglobin, in which there is a coinheritance of mutated b globin genes resulting in hemoglobin S and hemoglobin C.1 HbSC is less severe than the homozygous HbSS disease but some complications can be equally severe. Acute myocardial ischemia and infarction have been reported on rare occasions in children with HbSS disease. However, this complication is not reported in children with HbSC disease. We report one such case of acute myocardial ischemia in an adolescent with HbSC disease, in association with acute chest syndrome.

AB - Hemoglobin SC (HbSC) disease is the second most common inherited disorder of hemoglobin, in which there is a coinheritance of mutated b globin genes resulting in hemoglobin S and hemoglobin C.1 HbSC is less severe than the homozygous HbSS disease but some complications can be equally severe. Acute myocardial ischemia and infarction have been reported on rare occasions in children with HbSS disease. However, this complication is not reported in children with HbSC disease. We report one such case of acute myocardial ischemia in an adolescent with HbSC disease, in association with acute chest syndrome.

KW - hemoglobin SC

KW - myocardial ischemia

KW - sickle cell crisis

UR - http://www.scopus.com/inward/record.url?scp=84896728408&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=84896728408&partnerID=8YFLogxK

U2 - 10.1097/01.mph.0000438028.87141.8c

DO - 10.1097/01.mph.0000438028.87141.8c

M3 - Article

C2 - 24322498

AN - SCOPUS:84896728408

VL - 36

SP - e97-e99

JO - Journal of Pediatric Hematology/Oncology

JF - Journal of Pediatric Hematology/Oncology

SN - 1077-4114

IS - 2

ER -