Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease: A case report

Marjorie Gayanilo; Michael Nares; Ofelia Alvarez; Sethuraman Swaminathan

doi:10.1097/01.mph.0000438028.87141.8c

Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease: A case report

Marjorie Gayanilo, Michael Nares, Ofelia Alvarez, Sethuraman Swaminathan

Pediatrics

Research output: Contribution to journal › Article › peer-review

Abstract

Hemoglobin SC (HbSC) disease is the second most common inherited disorder of hemoglobin, in which there is a coinheritance of mutated b globin genes resulting in hemoglobin S and hemoglobin C.1 HbSC is less severe than the homozygous HbSS disease but some complications can be equally severe. Acute myocardial ischemia and infarction have been reported on rare occasions in children with HbSS disease. However, this complication is not reported in children with HbSC disease. We report one such case of acute myocardial ischemia in an adolescent with HbSC disease, in association with acute chest syndrome.

Original language	English (US)
Pages (from-to)	e97-e99
Journal	Journal of Pediatric Hematology/Oncology
Volume	36
Issue number	2
DOIs	https://doi.org/10.1097/01.mph.0000438028.87141.8c
State	Published - Mar 1 2014

Keywords

hemoglobin SC
myocardial ischemia
sickle cell crisis

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Oncology
Hematology

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10.1097/01.mph.0000438028.87141.8c

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abstract = "Hemoglobin SC (HbSC) disease is the second most common inherited disorder of hemoglobin, in which there is a coinheritance of mutated b globin genes resulting in hemoglobin S and hemoglobin C.1 HbSC is less severe than the homozygous HbSS disease but some complications can be equally severe. Acute myocardial ischemia and infarction have been reported on rare occasions in children with HbSS disease. However, this complication is not reported in children with HbSC disease. We report one such case of acute myocardial ischemia in an adolescent with HbSC disease, in association with acute chest syndrome.",

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T1 - Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease

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AU - Gayanilo, Marjorie

AU - Nares, Michael

AU - Alvarez, Ofelia

AU - Swaminathan, Sethuraman

PY - 2014/3/1

Y1 - 2014/3/1

N2 - Hemoglobin SC (HbSC) disease is the second most common inherited disorder of hemoglobin, in which there is a coinheritance of mutated b globin genes resulting in hemoglobin S and hemoglobin C.1 HbSC is less severe than the homozygous HbSS disease but some complications can be equally severe. Acute myocardial ischemia and infarction have been reported on rare occasions in children with HbSS disease. However, this complication is not reported in children with HbSC disease. We report one such case of acute myocardial ischemia in an adolescent with HbSC disease, in association with acute chest syndrome.

AB - Hemoglobin SC (HbSC) disease is the second most common inherited disorder of hemoglobin, in which there is a coinheritance of mutated b globin genes resulting in hemoglobin S and hemoglobin C.1 HbSC is less severe than the homozygous HbSS disease but some complications can be equally severe. Acute myocardial ischemia and infarction have been reported on rare occasions in children with HbSS disease. However, this complication is not reported in children with HbSC disease. We report one such case of acute myocardial ischemia in an adolescent with HbSC disease, in association with acute chest syndrome.

KW - hemoglobin SC

KW - myocardial ischemia

KW - sickle cell crisis

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Acute myocardial ischemia in association with acute respiratory acidosis in hemoglobin SC disease: A case report

Abstract

Keywords

ASJC Scopus subject areas

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