A patient with an epignathus

management of a large oropharyngeal teratoma in a newborn.

Keyoumars Izadi, Meghan Smith, Morad Askari, David Hackam, Aziz Abdul Hameed, James P. Bradley

Research output: Contribution to journalArticle

30 Citations (Scopus)

Abstract

An epignathus is an oropharyngeal teratoma composed of cells from ectodermal, mesodermal, and endodermal layers. Epignathi that arise from the palate or pharynx and protrude from the mouth result in life-threatening airway obstruction and usually cause asphyxiation shortly after birth. In our reported case, an antenatal ultrasound diagnosis allowed for preparation of an ex utero intrapartum treatment (EXIT) procedure. A tracheostomy was performed at birth with maternal-fetal blood flow still intact through the umbilical cord. Debulking of the large extraoral portion of the tumor, followed by complete intraoral resection, was performed. Masseteric function and swallowing slowly improved over several weeks. Cleft palate repair is planned at 10 months of age. In the following report, the histology, classification, and pathogenesis of these "parasitic" tumors are reviewed.

Original languageEnglish
Pages (from-to)468-472
Number of pages5
JournalThe Journal of craniofacial surgery
Volume14
Issue number4
StatePublished - Jul 1 2003
Externally publishedYes

Fingerprint

Teratoma
Parturition
Newborn Infant
Palate
Umbilical Cord
Tracheostomy
Asphyxia
Cleft Palate
Airway Obstruction
Deglutition
Pharynx
Prenatal Diagnosis
Fetal Blood
Mouth
Neoplasms
Histology
Mothers
Therapeutics

ASJC Scopus subject areas

  • Surgery

Cite this

Izadi, K., Smith, M., Askari, M., Hackam, D., Hameed, A. A., & Bradley, J. P. (2003). A patient with an epignathus: management of a large oropharyngeal teratoma in a newborn. The Journal of craniofacial surgery, 14(4), 468-472.

A patient with an epignathus : management of a large oropharyngeal teratoma in a newborn. / Izadi, Keyoumars; Smith, Meghan; Askari, Morad; Hackam, David; Hameed, Aziz Abdul; Bradley, James P.

In: The Journal of craniofacial surgery, Vol. 14, No. 4, 01.07.2003, p. 468-472.

Research output: Contribution to journalArticle

Izadi, K, Smith, M, Askari, M, Hackam, D, Hameed, AA & Bradley, JP 2003, 'A patient with an epignathus: management of a large oropharyngeal teratoma in a newborn.', The Journal of craniofacial surgery, vol. 14, no. 4, pp. 468-472.
Izadi K, Smith M, Askari M, Hackam D, Hameed AA, Bradley JP. A patient with an epignathus: management of a large oropharyngeal teratoma in a newborn. The Journal of craniofacial surgery. 2003 Jul 1;14(4):468-472.
Izadi, Keyoumars ; Smith, Meghan ; Askari, Morad ; Hackam, David ; Hameed, Aziz Abdul ; Bradley, James P. / A patient with an epignathus : management of a large oropharyngeal teratoma in a newborn. In: The Journal of craniofacial surgery. 2003 ; Vol. 14, No. 4. pp. 468-472.
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